Perioperative management of the patient with pheochromocytoma and Von Recklinghausen's disease
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Neurofibromatosis 1
Hemodynamic monitoring
Perioperative Period

How to Cite

Molina Valencia, J. L., Barragán-Briceño, T., Restrepo-Moreno, M., Vásquez-Arango, J. ., & Toro-Vásquez, J. P. (2023). Perioperative management of the patient with pheochromocytoma and Von Recklinghausen’s disease. Revista Colombiana De Endocrinología, Diabetes &Amp; Metabolismo, 10(4).


Introduction: In patients with neurofibromatosis type 1 the prevalence of pheochromocytoma is high, the risk of having a pheochromocytoma is 10 times higher than in the general population.

Objective: Describe the case of a patient with infrequent pathologies that requires the assistance of experts for its management before and in the follow-up after surgery.

Presentation of the case: Male, 38 years old with a history of NF1, evaluated for 4 months of headache, abdominal pain and difficult-to-control arterial hypertension. A diagnosis of pheochromocytoma was made and adrenalectomy was defined with perioperative hospitalization to control blood pressure levels with alpha and beta blockers.

Discussion: The management of pheochromocytoma is surgical resection. For the surgical procedure, patients must receive alpha blockade at least 10 days before the procedure and beta blockers 3 days before. Catecholamine crises can occur intraoperatively due to mechanical stress of the tumor. when being manipulated, psychological stress and medication.

Conclusion: Surgical treatment is the choice and must be performed by an interdisciplinary group to ensure adequate control of blood pressure figures in the perioperative period and thus avoid complications.
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