Reporte de caso y revisión breve Paciente con un caso poco frecuente de hta: pseudohipoaldosteronismo tipo 2 o síndrome de Gordon
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hipertensión arterial secundaria
pseudo- hipoaldosteronismo tipo 2
síndrome de Gordon
Secondary hypertension
pseudohypoaldosteronism type 2
Gordon syndrome

How to Cite

González Clavijo, A. ´María, Fierro Maya, L. F., Franco Vega, R., & Caminos Pinzón, J. E. (2017). Reporte de caso y revisión breve Paciente con un caso poco frecuente de hta: pseudohipoaldosteronismo tipo 2 o síndrome de Gordon. Revista Colombiana De Endocrinología, Diabetes &Amp; Metabolismo, 1(1), 42–46.


Describimos el caso de una paciente con diagnóstico de hipertensión arterial (HTA) desde los 14 años de edad con frecuentes hospitalizaciones por crisis hipertensivas que no se lograban controlar con dosis crecientes de antihipertensivos. Se le realizaron múltiples estudios para HTA secundaria pero lo único anormal fue la presencia de hipercaliemia y acidosis metabólica. Con estos hallazgos se hizo la impresión diagnóstica de pseudohipoaldosteronismo tipo 2 o síndrome de Gordon y se instauró tratamiento con hidroclorotiazida en dosis crecientes con lo cual se lograron estabilizar las cifras tensionales y mejorar la hipercaliemia.

We describe the case of a patient diagnosed with hypertension at age 14 with multiple hospitalizations for hypertensive crisis. Despite increasing doses of antihypertensive drugs, her blood pressure was not controlled. Attempts were made to rule out secondary hypertension, but to no avail, except for the presence of hyperkalemia and metabolic acidosis. With these results, the diagnostic impression was of Type 2 pseudohypoaldosteronism or Gordon’s syndrome. The patient was treated with thiazides at increasing doses, which succeeded in stabilizing her blood pressure and improving hyperkalemia.
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