Tumor pardo espinal como primera manifestación de un hiperparatiroidismo primario: revisión sistemática de la literatura y reporte de un caso
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Keywords

tumor pardo espinal
hiperparatiroidismo primario
Osteitis Fibrosa Cystica
Primary Hyperparathyroidism
Bone Neoplasms

How to Cite

Quevedo-Vélez, C., Castaño-Lopera, V., Espinosa-De La Ossa, C., Moncayo-Viveros, J. G., & Builes-Montaño, C. E. (2017). Tumor pardo espinal como primera manifestación de un hiperparatiroidismo primario: revisión sistemática de la literatura y reporte de un caso. Revista Colombiana De Endocrinología, Diabetes &Amp; Metabolismo, 4(3), 20–24. https://doi.org/10.53853/encr.4.3.132

Abstract

Los tumores pardos son una forma rara de manifestación del hiperparatiroidismo; pueden afectar cualquier hueso del cuerpo como lesiones únicas o múltiples, pero es bastante inusual que afecten la columna. El compromiso espinal se acompaña de síntomas neurológicos severos, y en la mayoría de los casos reportados, se ha recurrido a la intervención neuroquirúrgica de la lesión para resolver este tipo de manifestaciones clínicas.
Presentamos el caso de un tumor pardo espinal, como primera manifestación de un hiperparatiroidismo primario, que fue tratado solo con paratiroidectomía y que no requirió ninguna intervención neuroquirúrgica para obtener una recuperación completa de los síntomas neurológicos.
La resección del tumor, busca mejorar los síntomas motores por compresión o establecer un diagnóstico histológico por sospecha de malignidad. Sin embargo, debido a que los tumores pardos en el hiperparatiroidismo primario ocurren por la acción de la paratohormona, estos podrían desaparecer completamente, normalizando los niveles de dicha hormona en sangre. En algunos casos se podría contemplar la posibilidad de no intervenir la lesión espinal y resolver inicialmente el hiperparatiroidismo.

Abstract

Brown tumors are a rare form of manifestation of a primary hyperparathyroidism; They can affect any bone in the body as single or multiple lesions, but the appearance of these lesions in the spine is quite unusual. When spinal involvement occurs, it is accompanied by severe neurological symptoms and in most of reported cases, the neurosurgical intervention of the lesion has been used to resolve this type of clinical manifestations.
We present the case of a spinal brown tumor as the first manifestation of a primary hyperparathyroidism that was treated with parathyroidectomy alone and did not require any neurosurgical intervention to obtain a complete recovery of the neurological symptoms.
Resection of the tumor, seeks to improve motor symptoms by compression or establish a histological diagnosis for suspected malignancy. However, because brown tumors occur due to the action of the paratohormone, a complete disappearance of the lesion could occur as the hormone levels normalizes. In some cases, the possibility of not intervening the spinal lesion could be contemplated and initially resolve the hyperparathyroidism.

https://doi.org/10.53853/encr.4.3.132
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